The tumour is most commonly seen on the trunk, followed by the shoulder or limbs and least commonly on the face or neck.
The tumour is slow growing and eventually grows outwards from the skin to form multiple nodules that are pink, violet-red or skin coloured. Another presentation is that of a firm scar.
The lesions starts off quite small between 2-5cm however it can be up to 25cm by the time it is discovered and diagnosed. It rarely spreads to other parts of the body.